Diagnosis of Human Prion Disease Using Real-Time Quaking-Induced Conversion Testing of Olfactory Mucosa and Cerebrospinal Fluid Samples
JAMA Neurol 74:155-162,144, Bongianni, M.,et al, 2017
Kuru in the 21st Century--An Acquired Human Prion Disease With Very Long Incubation Periods
Lancet 367:2068-2074, Collinge,J.,et al, 2006
Transmissible Spongiform Encephalopathies
Lancet 363:51-61, Collins,S.J.,et al, 2004
Neurodegenerative Diseases and Prions
NEJM 344:1516-1526,1548, Prusiner,S.B., 2001
14-3-3 Testing in Diagnosing Creutzfeldt-Jakob Disease
Neurol 55:514-516, Lemstra,A.W. et al, 2000
Risk of Transmission of Bovine Spongiform Encephalopathy to Humans in the United States, Report of the Council on Scientific Affairs
JAMA 281:2330-2339, Tan,L.,et al, 1999
Detection of 14-3-3 Protein in Cerebrospinal Fluid Supports Dx of Creutzfeldt-Jakob Disease
Ann Neurol 43:32-40, Zerr,I.,et al, 1998
Creutzfeldt-Jakob Disease and Related Transmissible Spongiform Encephalopathies
NEJM 339:1994-2004, Johnson,R.T. & Gibbs,Jr.,C.J., 1998
The 14-3-3 Brain Protein and Transmissible Spongiform Encephalopathy
NEJM 336:873-875, Moussavian,M.,et al, 1997
The Risk of Bovine Spongiform Encephalopathy ('Mad Cow Disease') to Human Health
JAMA 278:1008-1011, Brown,P., 1997
New Variant Creutzfeldt-Jakob Disease:Neurological Features and Diagnostic Tests
Lancet 350:903-907, Zeidler,M.,et al, 1997
Transmissible Spongiform Encephalopathies
NEJM 337:1821-1828, Haywood,A.M., 1997
Bovine Spongiform Encephalopathy and Creutzfeldt-Jakob Disease
BMJ 312:790-791, Brown,P., 1996
A New Variant of Creutzfeldt-Jakob Disease in the UK
Lancet 347:921-925, 915, 916, 91796., Will,R.G.,et al, 1996
The 14-3-3 Brain Protein in Cerebrospinal Fluid as a Marker for Transmissible Spongiform Encephalopathies
NEJM 335:924-930, 9631996., Hsich,G.,et al, 1996
Creutzfeldt-Jakob Disease and Bovine Spongiform Encephalopathy:Any Connection?
BMJ 311:1415-1421, Almond,J.W., 1995
Human Prion Diseases
Ann Neurol 35:385-395, Prusiner,S.B.&Hsiao,K.K., 1994
The Spongiform Encephalopathies, Editorial
JNNP 54:761-763, Will,R.G., 1991
Viral Infections of the Nervous System, Chronic Meningitis, and Prior Diseases, Creutzfeldt-Jakob Disease (Subacute Spongiform Encephalopathy)
Adams & Victors Principles of Neurology, Chp 33, pg 769, Ropper, A.H.,et al, 2014
Cortical Restricted Diffusion as the Predominant MRI Finding in Sporadic Creutzfeldt-Jakob Disease
Acta Radiologica 52:336-339, Talbott,S.D.,et al, 2011
Transmissible Spongiform Encephalopathy in the 21st Century: Neuroscience for the Clinical Neurologist
Neurol 70:713-722, Brown,P., 2008
Clinicopath conf., Human Prion Disease, Sporadic CJD
Neurol 69:1881-1887, Geschwind,M.D., et al, 2007
Progressive Aphasia with Rapidly Progressive Dementia in a 49 Year Old Woman
JNNP 66:238-243, Greene,J.D.W.,et al,, 1999
Surgical Treatment and Risk of Sporadic Creutzfeldt-Jakob Disease:A Case-Control Study
Lancet 353:693-697, Collins,S.,et al, 1999
Rapid Spongiform Degeneration of the Cerebrum and Cerebellum in Creutzfeldt-Jakob Encephalitis:Serial MR Findings
AJNR 18:583-586, Tzeng,B-C.,et al, 1997
MRI of Creutzfeldt-Jakob Disease:Asymmetric High Signal Intensity of the Basal Ganglia
Neurol 45:1932-1933, Yoon,S.S.,et al, 1995
Human Spongiform Encephalopathy:The NIH Series of 300 Cases of Experimentally Transmitted Disease
Ann Neurol 35:513-529, Brown,P.,et al, 1994
Creutzfeldt-Jakob Disease and Other Transmissible Spongiform Encephalopathies
Ed, F. O. Bastian, Mosby Year Book, St. Louis 9:153, Maertens,P.&Quindlen,E.A., 1991
Transmission of Alpers'Disease (Chr Prog Encephalopathy) Produces Exper Creutzfeldt-Jakob Disease in Hamsters
Neurol 39:615-621, Manuelidis,E.E.,et al, 1989
Prions & Neurodegenerative Diseases
NEJM 317:1571-1581, 15971987., Prusiner,S.B., 1987
Diagnosis of Creutzfeldt-Jakob Disease by Western Blot Identification of Marker Protein in Human Brain Tissue
NEJM 314:547-551, Brown,P.,et al, 1986
Creutzfeldt-Jakob Disease after Administration of Human Growth Hormone
Lancet 2:244-246, Powell-Jackson,J.,et al, 1985
Subacute Spongiform Encephalopathy (Creutzfeldt-Jakob Disease) with Amyloid Angiopathy
JNNP 48:1175-1178, Keohane,C.,et al, 1985
Clinical Pathologic Conference, Creutzfeldt-Jakob Disease, (Case record 43-1977)
NEJM 297:930, Scully,R.E.,et al, 1977
Clinical, Neuroimaging, and Pathologic Features of Progressive Nonfluent Aphasia
Ann Neurol 39:166-173, Turner,R.S.,et al, 1996
Leigh Syndrome:Clinical Features and Biochemical DNA Abnormalities
Ann Neurol 39:343-351, Rahman,S.,et al, 1996
Canavan Disease:From Spongy Degeneration to Molecular Analysis
J Pediatr 127:511-517, Matalon,R.,et al, 1995
The Pathology and Nosology of Primary Progressive Aphasia
Neurol 44:2065-2072, Kertesz,A.,et al, 1994
Progressive Language Disorder Due to Lobar Atrophy
Ann Neurol 31:174-183, Snowden,J.S.,et al, 1992
Progressive Aphasia without Dementia:Two Cases with Focal Spongiform Degeneration
Ann Neurol 22:527-532, Kirshner,H.S.,et al, 1987